Ectopia cordis

Hong Kong Med J. 2013 Oct;19(5):447-50. doi: 10.12809/hkmj133737.


We report on a preterm male newborn with complete ectopia cordis associated with Cantrell's syndrome. The neonate had an ectopia cordis involving defects of the lower sternum, supraumbilical abdominal wall, anterior portion of the diaphragm, and diaphragmatic portion of the pericardium associated with complex congenital heart defects. The infant died shortly after birth. We discuss this case and review the literature.

Keywords: Abdominal wall; Ectopia cordis; Heart defects, congenital; Pentalogy of Cantrell.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / physiopathology*
  • Ectopia Cordis / etiology
  • Ectopia Cordis / physiopathology*
  • Fatal Outcome
  • Female
  • Humans
  • Infant, Newborn
  • Male
  • Pentalogy of Cantrell / physiopathology*
  • Pregnancy
  • Young Adult