Retropharyngeal phlegmon in Rosai Dorfman disease

Int J Pediatr Otorhinolaryngol. 2014 Feb;78(2):373-6. doi: 10.1016/j.ijporl.2013.11.019. Epub 2013 Nov 25.


Rosai Dorfman disease (RD), also known as sinus histiocytosis with massive lymphadenopathy (SHML), is a benign histiocytic proliferative condition of unsubstantiated etiology that most often presents as bilateral painless cervical lymphadenopathy. Head and neck manifestations of RD are diverse but most commonly present as massive cervical lymphadenopathy. Interestingly, a retropharyngeal fluid collection has never been described as a sequelae of RD. Our objective is to present a novel case of a 9-year old female with RD that suffered from recurrent retropharyngeal phlegmon and to discuss diagnostic and treatment recommendations for this disease process.

Keywords: Extranodal; Phlegmon; Retropharyngeal; Rosai Dorfman.

Publication types

  • Case Reports

MeSH terms

  • Cellulitis / diagnostic imaging*
  • Cellulitis / pathology
  • Cellulitis / surgery
  • Child
  • Female
  • Histiocytosis, Sinus / diagnostic imaging*
  • Histiocytosis, Sinus / pathology
  • Histiocytosis, Sinus / surgery
  • Humans
  • Pharyngeal Diseases / diagnostic imaging*
  • Pharyngeal Diseases / pathology
  • Pharyngeal Diseases / surgery
  • Recurrence
  • Tomography, X-Ray Computed