Lymphocytoma cutis--case report

An Bras Dermatol. 2013 Nov-Dec;88(6 Suppl 1):128-31. doi: 10.1590/abd1806-4841.20132320.

Abstract

We describe a clinical case involving a 62-year-old white male, diagnosed with lymphocytoma cutis (Spiegler-Fendt sarcoid) in the cephalic segment. The diagnosis was carried out by pathological study and confirmed by immunohistochemical panel: evidence of polyclonality. Phototherapy sessions were suggested as treatment (13 PUVA sessions, with an accumulated dose of 58.65 J/cm2 ). The improvement was partial. Thus, infiltration of triamcinolone was opted for (one intralesional infiltration every 3 weeks). After 5 sessions, satisfactory improvement was observed: regression of nearly all the lesions.

Relatamos um caso de um paciente de 62 anos, branco e com diagnóstico de linfocitoma cutis (Sarcoide de Spigler-Fendt) em segmento cefálico. O diagnóstico foi confirmado pelo histopatológico e reafirmado pelo painel imuno-histoquímico: evidência de policlonalidade. Sessões de fototerapia foram propostas como tratamento: 13 sessões de PUVA cuja dose acumulada foi de 58.65 J/cm2); a melhora foi parcial. Optado, então, por infiltrações de triancinolona (uma infiltração intralesional a cada 3 semanas). Na quinta sessão, satisfatória melhora já podia ser evidenciada: regressão de quase todas as lesões.

Publication types

  • Case Reports

MeSH terms

  • Biopsy
  • Glucocorticoids / therapeutic use
  • Humans
  • Immunohistochemistry
  • Male
  • Middle Aged
  • PUVA Therapy
  • Pseudolymphoma / drug therapy
  • Pseudolymphoma / pathology*
  • Skin / pathology
  • Skin Diseases / drug therapy
  • Skin Diseases / pathology*
  • Time Factors
  • Treatment Outcome
  • Triamcinolone / therapeutic use

Substances

  • Glucocorticoids
  • Triamcinolone