Uterine sarcomas are rare aggressive mesenchymal tumours with limited prognosis. They encompass various histological subtypes such leiomyosarcoma, endometrial stromal sarcoma and undifferentiated sarcomas with different surgical and medical strategies. Current evidence of surgery, adjuvant and palliative therapy is reported.
Keywords: chemotherapy; endometrial stromal sarcoma; surgery; uterine leiomyosarcoma; uterine sarcoma.