Is cystic fibrosis respiratory epithelium characterized by a single defect (Cl-) or multiple ion transport defects?

Prog Clin Biol Res. 1987:254:89-100.
No abstract available

Publication types

  • Review

MeSH terms

  • Cell Membrane Permeability
  • Chlorides / metabolism*
  • Cystic Fibrosis / metabolism*
  • Epithelium / metabolism
  • Humans
  • Ion Channels / metabolism*
  • Lung / metabolism
  • Sodium / metabolism*

Substances

  • Chlorides
  • Ion Channels
  • Sodium