Pulmonary atresia with ventricular septal defect and pulmonary sequestration

Asian Cardiovasc Thorac Ann. 2013 Aug;21(4):460-3. doi: 10.1177/0218492312456692. Epub 2013 Jul 1.


A 5-day-old girl who had pulmonary atresia with ventricular septal defect, patent ductus arteriosus, intralobar pulmonary sequestration of the right lower lobe, and retroesophageal innominate vein, was referred to our institution. We successfully performed a systemic-to-pulmonary shunt. During cardiopulmonary bypass, the arteries supplying the sequestrated lung were ligated above the diaphragm through the median sternotomy, without a thoracotomy. The postoperative course was uneventful, and we avoided the potential complications of lung infection and ventricular overload.

Keywords: Multiple abnormalities; bronchopulmonary sequestration; patent ductus arteriosus; pulmonary atresia with ventricular septal defect.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Blood Vessel Prosthesis Implantation
  • Brachiocephalic Veins / abnormalities
  • Bronchopulmonary Sequestration* / diagnosis
  • Bronchopulmonary Sequestration* / surgery
  • Cardiac Surgical Procedures
  • Cardiopulmonary Bypass
  • Ductus Arteriosus, Patent / diagnosis
  • Female
  • Heart Septal Defects* / diagnosis
  • Heart Septal Defects* / surgery
  • Humans
  • Infant, Newborn
  • Multidetector Computed Tomography
  • Phlebography / methods
  • Pulmonary Atresia* / diagnosis
  • Pulmonary Atresia* / surgery
  • Sternotomy
  • Treatment Outcome

Supplementary concepts

  • Pulmonary Atresia With Ventricular Septal Defect