Objective: The objective was to document and describe the clinical features of a hemangioblastoma arising from a submandibular gland.
Methods: A case report of a 63-year-old man with a right submandibular gland hemangioblastoma.
Results: Submandibular gland excision and histological examination revealed a hemangioblastoma. Subsequent evaluation with imaging studies found no association with von Hippel-Lindau disease.
Conclusion: We report the first presentation of a hemangioblastoma arising in a salivary gland. Further evaluation of patients with a hemangioblastoma is recommended given the neoplasms' association with von Hippel-Lindau disease.