Hypertrophic cardiomyopathy with right ventricular outflow tract and left ventricular intracavitary obstruction

Echocardiography. 2014 May;31(5):682-5. doi: 10.1111/echo.12543. Epub 2014 Mar 20.

Abstract

Obstruction of the right ventricular outflow tract (RVOT) is a rare finding in hypertrophic cardiomyopathy (HCM) patients unlike left ventricular outflow tract (LVOT) obstruction. Although there are guidelines that aid in clinical decision making in patients with LVOT obstruction, there are none addressing RVOT obstruction. As RVOT obstruction may pose serious clinical implications similar to LVOT obstruction, appropriate medical and surgical management is very important. A unique phenotype of HCM with RVOT obstruction in conjunction with left ventricle (LV) intracavitary obstruction is discussed.

Keywords: biventricular obstruction; hypertrophic cardiomyopathy; left ventricular intracavitary obstruction; right ventricular outflow tract obstruction.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cardiomyopathy, Hypertrophic / complications
  • Cardiomyopathy, Hypertrophic / diagnostic imaging*
  • Cardiomyopathy, Hypertrophic / physiopathology
  • Diagnosis, Differential
  • Echocardiography, Three-Dimensional / methods*
  • Female
  • Follow-Up Studies
  • Heart Ventricles / diagnostic imaging*
  • Heart Ventricles / physiopathology
  • Humans
  • Ventricular Function, Left / physiology*
  • Ventricular Function, Right / physiology*
  • Ventricular Outflow Obstruction / diagnostic imaging
  • Ventricular Outflow Obstruction / etiology*
  • Ventricular Outflow Obstruction / physiopathology