Unusual variant of tetralogy of Fallot with pulmonary atresia: a right pulmonary artery from the ascending aorta and a coronary-to-left pulmonary artery collateral

Cardiol Young. 2015 Mar;25(3):554-6. doi: 10.1017/S1047951114000341. Epub 2014 Apr 3.


We present the case of a newborn with tetralogy of Fallot and pulmonary atresia, with a right pulmonary artery from the ascending aorta, and a left pulmonary artery arising from the right coronary artery via an indirect aortopulmonary collateral. The embryogenesis of this unusual combination of pulmonary blood supply has significant implications when considering normal migration of the aortopulmonary septum.

Keywords: aortic arches.

Publication types

  • Case Reports

MeSH terms

  • Aorta / abnormalities
  • Collateral Circulation*
  • Coronary Vessels / pathology*
  • Echocardiography, Doppler, Color*
  • Humans
  • Infant, Newborn
  • Male
  • Pulmonary Artery / abnormalities*
  • Pulmonary Atresia / diagnostic imaging
  • Pulmonary Atresia / pathology*
  • Tetralogy of Fallot / diagnostic imaging
  • Tetralogy of Fallot / pathology*