Cystic interstitial lung diseases: recognizing the common and uncommon entities

Curr Probl Diagn Radiol. May-Jun 2014;43(3):115-27. doi: 10.1067/j.cpradiol.2014.01.001.


Cystic lung diseases present a considerable diagnostic challenge because they are less frequently encountered in clinical practice and high-resolution computed tomography findings are often similar in many of these diseases. Here, we review the high-resolution computed tomography findings of cystic lung diseases and their mimics and provide a systematic approach to their diagnosis. Specific diseases that are discussed include pulmonary Langerhans cell histiocytosis, lymphangioleiomyomatosis, Birt-Hogg-Dubé syndrome, lymphocytic interstitial pneumonia, and light chain deposition disease.

Publication types

  • Review

MeSH terms

  • Birt-Hogg-Dube Syndrome / diagnostic imaging*
  • Cysts / diagnostic imaging
  • Cysts / pathology*
  • Diagnosis, Differential
  • Emphysema / pathology
  • Histiocytosis, Langerhans-Cell / diagnostic imaging*
  • Humans
  • Lung / pathology*
  • Lung Diseases / diagnostic imaging*
  • Lung Diseases, Interstitial / diagnostic imaging*
  • Lymphangioleiomyomatosis / diagnostic imaging*
  • Tomography, X-Ray Computed

Supplementary concepts

  • Cystic Disease Of Lung
  • Lymphoid Interstitial Pneumonia