Fontan operation in a paediatric patient with a history of Takotsubo cardiomyopathy

Interact Cardiovasc Thorac Surg. 2014 Aug;19(2):326-8. doi: 10.1093/icvts/ivu108. Epub 2014 May 13.


Takotsubo cardiomyopathy is very rare in the paediatric population and has not been described in a single-ventricle patient yet. We report the case of a 4-year old boy with a history of Takotsubo cardiomyopathy in whom we performed a Fontan operation. After coil embolization of the minor aortopulmonary collateral arteries, the patient developed Takotsubo cardiomyopathy. His cardiac function largely recovered over 3 months. He subsequently progressed to a Fontan operation and was weaned uneventfully off cardiopulmonary bypass, on minimal doses of dopamine and milrinone; he was sedated using a dexmedetomidine infusion and a midazolam bolus. There were no signs of recurrent Takotsubo cardiomyopathy over the subsequent 2 years.

Keywords: Fontan candidate; Paediatric patient; Takotsubo cardiomyopathy.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Electrocardiography
  • Embolization, Therapeutic / adverse effects*
  • Fontan Procedure*
  • Heart Defects, Congenital / diagnosis
  • Heart Defects, Congenital / surgery
  • Heart Defects, Congenital / therapy*
  • Humans
  • Male
  • Recovery of Function
  • Stroke Volume
  • Takotsubo Cardiomyopathy / diagnosis
  • Takotsubo Cardiomyopathy / etiology*
  • Takotsubo Cardiomyopathy / physiopathology
  • Takotsubo Cardiomyopathy / therapy
  • Treatment Outcome
  • Ventricular Function, Left