Congenital complete absence of pericardium in a young woman with non-specific symptoms

Rev Port Cardiol. 2014 Apr;33(4):249.e1-5. doi: 10.1016/j.repc.2013.10.015. Epub 2014 May 13.


Congenital absence of the pericardium is a very rare entity that is usually asymptomatic and hence difficult to diagnose. However, cases of sudden death have been reported in patients with partial pericardial defects (even asymptomatic ones), and such patients require surgical treatment. We report the case of a 17-year-old patient with complete pericardial agenesis (diagnosed by chance during a cardiological consultation) and briefly review the radiological findings of this entity.

Keywords: Absence; Ausência; Image; Imagem; Magnetic resonance; Multislice computed tomography; Pericardium; Pericárdio; Ressonância magnética; Tomografia computadorizada de múltiplos detectores.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Congenital Abnormalities / diagnosis
  • Female
  • Humans
  • Pericardium / abnormalities*