Cor triatriatum sinister

Multimed Man Cardiothorac Surg. 2014 May 30:2014:mmu005. doi: 10.1093/mmcts/mmu005. Print 2014.


The cor triatriatum sinister is an uncommon congenital cardiac anomaly and reports in the literature are limited. It is often associated with other cardiac malformations, such as atrial septal defect, transposition of the great arteries, tetralogy of Fallot or atrioventricular septal defect. We present here a 6-year old boy who was diagnosed with cor triatriatum sinister, initially showing symptoms similar to mitral valve stenosis and congestive heart failure, and who underwent subsequent surgical correction using a left atrial approach. The fibromuscular membrane, separating the pulmonary veins from the mitral valve, was completely resected and postoperative echocardiography showed unobstructed pulmonary venous flow.

Keywords: Congenital cardiac surgery; Cor triatriatum; Left heart lesions; Pulmonary hypertension; Pulmonary veins.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Cardiopulmonary Bypass / adverse effects
  • Cardiopulmonary Bypass / methods
  • Child
  • Cor Triatriatum* / diagnosis
  • Cor Triatriatum* / physiopathology
  • Cor Triatriatum* / surgery
  • Echocardiography, Transesophageal / methods
  • Heart Arrest, Induced* / adverse effects
  • Heart Arrest, Induced* / methods
  • Heart Atria* / abnormalities
  • Heart Atria* / surgery
  • Heart Failure / diagnosis*
  • Humans
  • Hypertension, Pulmonary* / etiology
  • Hypertension, Pulmonary* / prevention & control
  • Intraoperative Care / methods
  • Male
  • Mitral Valve Stenosis / diagnosis*
  • Postoperative Complications / prevention & control*
  • Pulmonary Veins* / abnormalities
  • Pulmonary Veins* / surgery
  • Risk Adjustment
  • Sternotomy / adverse effects
  • Sternotomy / methods
  • Treatment Outcome