Association of Von Recklinghausen's Neurofibromatosis and Aqueduct Stenosis

Neurosurgery. 1989 Jan;24(1):99-101. doi: 10.1227/00006123-198901000-00017.

Abstract

We present 6 patients with a definite diagnosis of von Recklinghausen's neurofibromatosis. All of them had aqueductal stenosis and hydrocephalus requiring surgical intervention because of clinical signs of increased intracranial pressure confirmed by pressure measurements.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Adult
  • Cerebral Aqueduct / abnormalities*
  • Cerebral Aqueduct / diagnostic imaging
  • Cerebrospinal Fluid Shunts
  • Female
  • Humans
  • Hydrocephalus / diagnostic imaging
  • Hydrocephalus / etiology*
  • Hydrocephalus / surgery
  • Male
  • Neurofibromatosis 1 / complications*
  • Tomography, X-Ray Computed