Isolated autonomic failure without evident somatic polyneuropathy in AL amyloidosis

Amyloid. 2014 Sep;21(3):218-20. doi: 10.3109/13506129.2014.935321. Epub 2014 Jun 27.
No abstract available

Keywords: Amyloidosis; autoimmune autonomic ganglionopathy; nerve conduction study; neuropathy; orthostatic hypotension; pure autonomic failure.

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Aged
  • Amyloidosis / blood
  • Amyloidosis / complications
  • Amyloidosis / pathology*
  • Amyloidosis / therapy
  • Boronic Acids / therapeutic use
  • Bortezomib
  • Cyclophosphamide / therapeutic use
  • Dexamethasone / therapeutic use
  • Drug Therapy, Combination
  • Humans
  • Immunoglobulin Light Chains / blood
  • Immunoglobulin Light-chain Amyloidosis
  • Male
  • Middle Aged
  • Neural Conduction
  • Pure Autonomic Failure / blood
  • Pure Autonomic Failure / complications
  • Pure Autonomic Failure / pathology*
  • Pure Autonomic Failure / therapy
  • Pyrazines / therapeutic use
  • Stem Cell Transplantation
  • Transplantation, Autologous
  • Treatment Outcome

Substances

  • Boronic Acids
  • Immunoglobulin Light Chains
  • Pyrazines
  • Bortezomib
  • Dexamethasone
  • Cyclophosphamide