Nonatherosclerotic obstructive vascular diseases of the mesenteric and renal arteries

Clin Cardiol. 2014 Nov;37(11):700-6. doi: 10.1002/clc.22305. Epub 2014 Aug 6.

Abstract

Nonatherosclerotic vascular diseases of the mesenteric and renal arteries are considered to occur less frequently than those caused by occlusive atherosclerotic disease. However, when present, they pose a significant diagnostic and therapeutic challenge. Such disorders include fibromuscular dysplasia, median arcuate ligament syndrome, the renal nutcracker syndrome, and some forms of acute and chronic mesenteric ischemia (embolic and thrombotic). This is a heterogeneous group of disorders with substantial differences in the pathogenesis and diagnostic approaches to these diseases. We provide an overview of the pathogenesis, clinical presentation, diagnosis, and current management of fibromuscular dysplasia, median arcuate ligament syndrome, and the renal nutcracker syndrome.

Publication types

  • Review

MeSH terms

  • Celiac Artery / pathology
  • Constriction, Pathologic / complications
  • Constriction, Pathologic / diagnosis
  • Constriction, Pathologic / therapy
  • Fibromuscular Dysplasia / complications*
  • Fibromuscular Dysplasia / diagnosis
  • Fibromuscular Dysplasia / therapy
  • Humans
  • Mesenteric Arteries*
  • Mesenteric Vascular Occlusion / etiology*
  • Mesenteric Vascular Occlusion / therapy
  • Renal Artery Obstruction / etiology*
  • Renal Artery Obstruction / therapy
  • Renal Nutcracker Syndrome / complications*
  • Renal Nutcracker Syndrome / diagnosis
  • Renal Nutcracker Syndrome / therapy