Missed diagnosis of Behçet disease causing aortic regurgitation

Asian Cardiovasc Thorac Ann. 2016 Feb;24(2):167-8. doi: 10.1177/0218492314549199. Epub 2014 Sep 3.

Abstract

Aortic regurgitation is a rare and serious presentation of Behçet's disease. Here we describe a case of missed diagnosis of Behçet's disease in a 37-year-old man, causing symptomatic aortic regurgitation. Perioperative diagnosis of Behçet's aortitis is crucial because surgical intervention carries high reoperative morbidity and mortality.

Keywords: Aortic valve; Behçet syndrome; aortic valve insufficiency; aortitis; heart valve prosthesis implantation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Anti-Inflammatory Agents / administration & dosage
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / physiopathology*
  • Aortic Valve / surgery
  • Aortic Valve Insufficiency / diagnosis
  • Aortic Valve Insufficiency / etiology*
  • Aortic Valve Insufficiency / physiopathology
  • Aortic Valve Insufficiency / surgery
  • Behcet Syndrome / complications*
  • Behcet Syndrome / diagnosis
  • Behcet Syndrome / drug therapy
  • Delayed Diagnosis*
  • Heart Valve Prosthesis Implantation
  • Humans
  • Hydrocortisone / administration & dosage
  • Male
  • Predictive Value of Tests
  • Time Factors
  • Treatment Outcome
  • Ultrasonography

Substances

  • Anti-Inflammatory Agents
  • Hydrocortisone