Bilateral sensorineural hearing loss and labyrinthitis ossificans secondary to neurosarcoidosis

Cochlear Implants Int. 2014 Nov;15(6):337-40. doi: 10.1179/1754762814Y.0000000073. Epub 2014 Sep 5.


Objective: To report a case of cochlear ossification as a result of neurosarcoidosis in a patient with bilateral profound sensorineural hearing loss.

Study design: Case report: Setting University teaching hospital, tertiary referral center.

Patient: Forty-year-old man with neurosarcoidosis and bilateral profound sensorineural hearing loss. Intervention Unilateral cochlear implantation.

Outcome measure: Aided thresholds speech perception tests.

Results: Marked improvement in hearing following implant.

Conclusion: Patients with neurosarcoidosis are at risk of labyrinthitis ossificans. Early imaging of these patients is recommended and if early cochlear ossification is identified they should be offered rapid access to rehabilitation with a cochlear implant.

Keywords: Cochlear implant; Cochlear implantation; Hearing loss; Labyrinthitis ossificans; Neurosarcoidosis; Sensorineural hearing loss.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Central Nervous System Diseases / complications*
  • Cochlea / pathology
  • Cochlea / surgery
  • Cochlear Implantation
  • Early Diagnosis
  • Hearing Loss, Bilateral / diagnosis
  • Hearing Loss, Bilateral / etiology*
  • Hearing Loss, Bilateral / surgery
  • Hearing Loss, Sensorineural / diagnosis
  • Hearing Loss, Sensorineural / etiology*
  • Hearing Loss, Sensorineural / surgery
  • Humans
  • Labyrinthitis / etiology*
  • Male
  • Ossification, Heterotopic / etiology*
  • Ossification, Heterotopic / pathology
  • Sarcoidosis / complications*
  • Speech Perception

Supplementary concepts

  • Neurosarcoidosis