Crowned dens syndrome. A case report

Neuroradiol J. 2014 Sep;27(4):495-7. doi: 10.15274/NRJ-2014-10056. Epub 2014 Aug 29.

Abstract

Crystal deposition in the cervical spine around the odontoid process may lead to acute neck pain. This rare condition is called crowned dens syndrome and should be considered in the differential diagnosis of a possible etiology for fever, headache and cervical pain of unknown origin. The syndrome is often overlooked, thus leading to misdiagnosis, invasive and useless investigations (lumbar puncture, biopsy), inappropriate treatment (steroids, antibiotics, antiviral drugs) and prolonged hospitalization. This can be prevented by imaging, based on a cervical CT scan that allows an accurate diagnosis. The disease has a good prognosis and symptoms usually subside within a few weeks. We describe a patient with crowned dens syndrome which manifested with clinical (acute occipital headache) and radiographic (calcium deposits in the alar ligament) features. Our patient recovered in four days with symptomatic therapy.

Keywords: acute headache; alar ligament; calcium deposits; crowned dens syndrome.

Publication types

  • Case Reports

MeSH terms

  • Calcinosis / diagnostic imaging*
  • Female
  • Humans
  • Ligaments / diagnostic imaging*
  • Middle Aged
  • Neck Pain / diagnostic imaging*
  • Neck Pain / etiology
  • Odontoid Process / diagnostic imaging*
  • Spinal Diseases / complications
  • Spinal Diseases / diagnostic imaging*
  • Tomography, X-Ray Computed