Other vascular tumors

Abstract

Vascular tumors are rare in children and adults. Classification of these tumors has been difficult, especially in the pediatric population, due to the rarity of these lesions, the unusual morphologic appearance, their diverse clinical behavior, and no independent stratification for pediatric tumors. In 2013, The World Health Organization updated the classification of soft tissue vascular tumors. Pediatric tumors were not independently stratified and the terminology was mostly left unchanged, but the intermediate category of tumors was divided into locally aggressive and rarely metastasizing. These tumors are treated with multimodality therapy and therefore need the guidance of an interdisciplinary team for best care.

Keywords: Angiosarcoma; Benign vascular tumors; Epithelioid hemangioendothelioma (EHE); Intermediate vascular tumors; Kaposiform hemangioendothelioma (KHE); Kasabach–Merritt phenomenon (KMP); Malignant vascular tumors.