Alveolar Capillary Dysplasia With Misalignment of the Pulmonary Veins Associated With Aortic Coarctation and Intestinal Malrotation

J Perinatol. 2014 Oct;34(10):795-7. doi: 10.1038/jp.2014.94.

Abstract

Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare and lethal cause of refractory pulmonary hypertension of the newborn. We describe the clinical course of a neonate with refractory pulmonary hypertension diagnosed with ACD/MPV, aortic coarctation and other not previously reported associated malformations.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abnormalities, Multiple / diagnosis*
  • Abnormalities, Multiple / therapy
  • Aortic Coarctation / diagnostic imaging*
  • Aortic Coarctation / surgery
  • Autopsy
  • Cardiac Surgical Procedures / methods
  • Digestive System Abnormalities / diagnosis*
  • Digestive System Abnormalities / surgery
  • Disease Progression
  • Echocardiography, Doppler
  • Fatal Outcome
  • Humans
  • Hypertension, Pulmonary / diagnosis
  • Hypertension, Pulmonary / etiology
  • Infant, Newborn
  • Infant, Premature*
  • Intestinal Volvulus / diagnosis*
  • Intestinal Volvulus / surgery
  • Male
  • Persistent Fetal Circulation Syndrome / diagnosis*
  • Postoperative Complications / pathology
  • Rare Diseases
  • Respiratory Distress Syndrome, Newborn / diagnosis
  • Respiratory Distress Syndrome, Newborn / etiology

Supplementary concepts

  • Volvulus Of Midgut