Reversible obstructive hypertrophic cardiomyopathy in the Beckwith-Wiedemann syndrome

Pediatr Cardiol. Fall 1989;10(4):225-8. doi: 10.1007/BF02083298.

Abstract

Patients with the Beckwith-Wiedemann (B-W) syndrome have been reported to have an increased risk of congenital heart disease and of idiopathic cardiomegaly on chest x-ray. In the infant described here, reversible obstructive hypertrophic cardiomyopathy was documented and its relationship to the metabolic features of the B-W syndrome is discussed.

Publication types

  • Case Reports

MeSH terms

  • Beckwith-Wiedemann Syndrome / complications
  • Beckwith-Wiedemann Syndrome / diagnosis*
  • Beckwith-Wiedemann Syndrome / physiopathology
  • Cardiomegaly / diagnosis
  • Cardiomegaly / etiology
  • Cardiomegaly / physiopathology
  • Cardiomyopathy, Hypertrophic / complications
  • Cardiomyopathy, Hypertrophic / diagnosis*
  • Cardiomyopathy, Hypertrophic / physiopathology
  • Echocardiography, Doppler
  • Electrocardiography
  • Female
  • Follow-Up Studies
  • Humans
  • Hyperinsulinism / complications
  • Hyperinsulinism / physiopathology
  • Hypoglycemia / complications
  • Hypoglycemia / physiopathology
  • Infant, Newborn