[Intubation of a first time parturient with Klippel-Feil syndrome]

Ugeskr Laeger. 2014 Oct 6;176(41):V05130271.
[Article in Danish]

Abstract

We describe a case of a first time parturient with Klippel-Feil syndrome (KFS). KFS is defined by fusion of cervical vertebrae and the clinical triad of low posterior hairline, short wide neck and limited neck movement. KFS represents a complex challenging anaesthesiologic condition due to limited movement of the neck and the risk of irreversible neurologic sequelae if manipulated, as well as unpredictable effect of neuroaxial anaesthesia. We recommend awake fiberoptic intubation for airway management in this rare disorder and stress the necessity of early anaesthesiologic assessment in any cervical spine disorder that might need airway management.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cesarean Section
  • Female
  • Fiber Optic Technology*
  • Humans
  • Intubation, Intratracheal / methods*
  • Klippel-Feil Syndrome / complications*
  • Klippel-Feil Syndrome / pathology
  • Klippel-Feil Syndrome / physiopathology
  • Parity
  • Pregnancy
  • Pregnancy Complications / physiopathology
  • Pregnancy Outcome