Longitudinal vaginal septa with associated uterine anomalies: a case series

Female Pelvic Med Reconstr Surg. 2015 May-Jun;21(3):e23-6. doi: 10.1097/SPV.0000000000000140.

Abstract

Objectives: Vaginal septa and associated mullerian anomalies can be difficult to diagnose and manage. This case series intends to educate the readers about the benefits and limitations of radiologic techniques both for the investigation as well as for the surgical management of these cases. It also seeks to inform them about a unique combination of vaginal and uterine anomalies known as Herlyn-Werner-Wunderlich syndrome.

Cases: Three cases were discussed, each with a different presentation. All of the cases included obstructed right hemivagina and right renal agenesis. One case was associated with uterine septum and the other 2 cases were associated with uterus didelphys.

Conclusions: The correct diagnosis of associated uterine anomalies in patients presenting with vaginal septa can be challenging. Diagnosis solely based on imaging should be cautioned because of its limitations. Use of ultrasound in the operating room can be a valuable tool.

Publication types

  • Case Reports

MeSH terms

  • 46, XX Disorders of Sex Development / complications
  • 46, XX Disorders of Sex Development / diagnosis
  • 46, XX Disorders of Sex Development / surgery*
  • Abdominal Pain / etiology
  • Abdominal Pain / surgery
  • Adolescent
  • Congenital Abnormalities / diagnosis
  • Congenital Abnormalities / surgery*
  • Dysmenorrhea / etiology
  • Dysmenorrhea / surgery
  • Female
  • Humans
  • Kidney / abnormalities
  • Magnetic Resonance Imaging
  • Menorrhagia / etiology
  • Menorrhagia / surgery
  • Mullerian Ducts / abnormalities*
  • Mullerian Ducts / surgery
  • Urogenital Abnormalities / complications
  • Urogenital Abnormalities / diagnosis
  • Urogenital Abnormalities / surgery*
  • Uterine Hemorrhage / etiology
  • Uterine Hemorrhage / surgery
  • Uterus / abnormalities*
  • Uterus / surgery
  • Vagina / abnormalities*
  • Young Adult

Supplementary concepts

  • Mullerian aplasia
  • Renal Adysplasia
  • Uterine Anomalies