Bilateral cystoid macular edema with giant retinal achromic patch in a patient with tuberous sclerosis

Ophthalmic Surg Lasers Imaging Retina. 2014 Nov-Dec;45(6):602-5. doi: 10.3928/23258160-20141118-19.

Abstract

Retinal astrocytic hamartoma is the most common retinal finding in tuberous sclerosis and has been reported in association with cystoid macular edema. A retinal achromic patch is the second most common retinal finding in tuberous sclerosis. The authors report the first case of bilateral cystoid macular edema in which one the eyes does not have an identifiable retinal astrocytic hamartoma. They also describe a new retinal finding in tuberous sclerosis termed giant retinal achromic patch.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Anti-Inflammatory Agents, Non-Steroidal / therapeutic use
  • Drug Therapy, Combination
  • Female
  • Fluorescein Angiography
  • Glucocorticoids / therapeutic use
  • Humans
  • Ketorolac
  • Macular Edema / diagnosis
  • Macular Edema / drug therapy
  • Macular Edema / etiology*
  • Prednisolone / therapeutic use
  • Retinal Diseases / diagnosis
  • Retinal Diseases / etiology*
  • Retinal Pigment Epithelium / pathology*
  • Tomography, Optical Coherence
  • Tuberous Sclerosis / complications*
  • Tuberous Sclerosis / diagnosis
  • Vision Disorders / etiology
  • Visual Acuity

Substances

  • Anti-Inflammatory Agents, Non-Steroidal
  • Glucocorticoids
  • Prednisolone
  • Ketorolac