Treatment of congenital aniridia associated with subluxated infantile cataract

Med Arch. 2014 Jun;68(3):212-4. doi: 10.5455/medarh.2014.68.212-214. Epub 2014 May 31.

Abstract

A 5 year old boy was presented at Eye clinic University clinical center Tuzla with congenital aniridia in both eyes. Clinical examination revealed visual acuity of 0,08 without correction in right and 0.7 with -5.0 Dsph and -1.0 Dcyl Axx 109° in left eye. Opthalmologic examination showed bilateral aniridia associated with moderate cataract in the right and incipient cataract in the left eye. In the right eye, zonular weakness with incipient capsular displacement and esotropia of Δ6º, were noted. The patient underwent phacoemulsification, implantation of capsular tension ring and Artificial Iris implant in the capsular bag. Phacoemulsification went uneventful and early postoperative recovery was successful with no signs of aniridia-associated keratopathy development and normal values of intra ocular pressure. Patient was not motivated for operation of the left eye and it was corrected with soft contact lens. Six month after the operation visual acuity in the right eye improved to 0.9 with +1.25Dsph and maintained stable in left eye, with complete elimination of esotropia and signs of binocular vision restoration. Small incision cataract extraction with IOL and Artificial Iris implantation in one procedure can be used to correct congenital aniridia and cataract with significant visual function improvement.

Keywords: Artificial Iris; congenital aniridia; infantile cataract.

Publication types

  • Case Reports

MeSH terms

  • Aniridia / physiopathology
  • Aniridia / surgery*
  • Artificial Organs
  • Cataract / congenital*
  • Cataract Extraction*
  • Child, Preschool
  • Humans
  • Iris
  • Lens Implantation, Intraocular / methods*
  • Lens Subluxation / physiopathology
  • Lens Subluxation / surgery*
  • Male
  • Phacoemulsification*
  • Treatment Outcome
  • Visual Acuity