Evolutionary conserved Tyr169 stabilizes the β2-α2 loop of the prion protein

J Am Chem Soc. 2015 Mar 4;137(8):2948-57. doi: 10.1021/ja511568m. Epub 2015 Feb 20.

Abstract

Experimental evidence indicates that the primary structure of the β2-α2 loop region (residues 165-175) in mammalian prion proteins (PrP) influences the conversion from the cellular species (PrP(C)) to the β-sheet-rich aggregate. Here, we captured the transition of the β2-α2 loop from 310-helical turn to β turn by unbiased molecular dynamics simulations of the single-point mutant Y169G. Multiple conformations along the spontaneous transition of the mutant were then used as starting point for sampling of the free-energy surface of the wild type and other single-point mutants. Using two different methods for the determination of free energy profiles, we found that the barrier for the 310-helical turn to β turn transition of the wild type is higher by about 2.5 kcal/mol than for the Y169G mutant, which is due to favorable stacking of the aromatic rings of Y169 and F175, and a stable hydrogen bond between the side chains of Y169 and D178. The transition of the β2-α2 loop to β turn increases the solvent-exposure of the hydrophobic stretch 169-YSNQNNF-175. The simulations indicate that the strictly conserved Y169 in mammalian prion proteins stabilizes the 310-helical turn in the β2-α2 loop, thus hindering the conversion to an aggregation-prone conformation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Animals
  • Conserved Sequence*
  • Evolution, Molecular*
  • Humans
  • Kinetics
  • Mice
  • Molecular Dynamics Simulation
  • Peptide Fragments / chemistry
  • Prions / chemistry*
  • Protein Stability
  • Protein Structure, Secondary
  • Solvents / chemistry
  • Tyrosine*

Substances

  • Peptide Fragments
  • Prions
  • Solvents
  • Tyrosine