Abernethy syndrome, a rare cause of hypoxemia: A case report

Manoj Kumar Sahu; Akshay Kumar Bisoi; Naveen Chandrasekaran Chander; Sandeep Agarwala; Sandeep Chauhan

doi:10.4103/0974-2069.149526

Abernethy syndrome, a rare cause of hypoxemia: A case report

Ann Pediatr Cardiol. 2015 Jan-Apr;8(1):64-6. doi: 10.4103/0974-2069.149526.

Authors

Manoj Kumar Sahu¹, Akshay Kumar Bisoi¹, Naveen Chandrasekaran Chander¹, Sandeep Agarwala², Sandeep Chauhan³

Affiliations

¹ Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
² Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
³ Department of Cardiac Anesthesiology, All India Institute of Medical Sciences, New Delhi, India.

Abstract

Abernethy syndrome (congenital extrahepatic portosystemic shunt (CEPS II)) as an etiology of hepatopulmonary syndrome (HPS) is uncommon. The severe hypoxemia and its consequences become incapacitating for the patient. Early shunt closure resolves hypoxemia and clinical symptomatology and prevents irreversible changes in pulmonary vasculature.

Keywords: Abernethy syndrome; cyanosis; hepatopulmonary syndrome; portosystemic shunt.

Publication types

Case Reports