Two-stage correction of thumb adduction contracture in Freeman-Sheldon syndrome (craniocarpotarsal dysplasia)

J Hand Surg Am. 1989 Nov;14(6):937-40. doi: 10.1016/s0363-5023(89)80040-1.


Freeman-Sheldon syndrome is a rare congenital anomaly that is characterized by facial, hand, and foot deformities. We describe a female infant who had severe adduction contractures of the thumbs. A two-stage reconstruction was done. The first web space soft tissues were stretched with a transversely oriented external skeletal distractor, then a conventional first web space deepening and release was performed.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnostic imaging
  • Abnormalities, Multiple / rehabilitation
  • Abnormalities, Multiple / surgery*
  • Facial Bones / abnormalities
  • Female
  • Foot Deformities, Congenital / pathology
  • Hand Deformities, Congenital / diagnostic imaging
  • Hand Deformities, Congenital / rehabilitation
  • Hand Deformities, Congenital / surgery*
  • Humans
  • Infant, Newborn
  • Radiography
  • Thumb / abnormalities*
  • Thumb / diagnostic imaging
  • Thumb / surgery