A 20-year-old female presented with raised skin lesions all over the body since birth. Clinical examination revealed multiple pigmented macules and hyperkeratotic papules seen along Blaschko's lines over the face, neck, trunk and both lower limbs. Histopathological examination revealed hyperkeratosis with moderated acanthosis and uniform pigmentation over basal zone. Systemic examination was found to be normal. A diagnosis of systematised epidermal nevus in the absence of epidermal nevus syndrome was diagnosed and the patient was asked to undergo carbon dioxide laser mediated destruction of the skin lesions. The patient was also advised to be under surveillance for late onset neurological symptoms.
Keywords: Epidermal naevus; Epidermolytic; Verrucous.