Development of pulmonary arteriovenous malformations after modified Fontan operations

J Thorac Cardiovasc Surg. 1989 Dec;98(6):1045-50.


Two patients with complex cyanotic congenital heart disease and without previous Glenn anastomosis underwent modified Fontan operations. Postoperatively, pulmonary arteriovenous malformations developed that resulted in cyanosis from significant intrapulmonary right-to-left shunting. These malformations were detected by pulmonary angiograms and contrast echocardiograms. Pulmonary arteriovenous malformations may be a major cause of late clinical deterioration in patients treated with modified Fontan operations.

Publication types

  • Case Reports

MeSH terms

  • Arteriovenous Fistula / diagnostic imaging
  • Arteriovenous Fistula / etiology*
  • Cardiac Surgical Procedures / adverse effects*
  • Child, Preschool
  • Female
  • Heart Defects, Congenital / diagnostic imaging
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / surgery*
  • Humans
  • Infant
  • Male
  • Pulmonary Artery* / diagnostic imaging
  • Pulmonary Circulation
  • Pulmonary Veins* / diagnostic imaging
  • Radiography