Aorto-Tracheopexy in the Treatment of Hunter Syndrome

Ann Thorac Surg. 2015 Jun;99(6):2190-2. doi: 10.1016/j.athoracsur.2014.08.048.


Hunter syndrome is a multisystem genetic disease in which a significant proportion of morbidity and mortality arise from respiratory dysfunction. Notably, tracheal abnormalities in Hunter syndrome can compromise clinical stability, and management is primarily supportive. We describe here the first successful implementation of aorto-tracheopexy in a 19-year-old patient as a surgical strategy to resolve progressive respiratory deterioration.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aorta, Thoracic / surgery*
  • Bronchoscopy
  • Humans
  • Male
  • Mucopolysaccharidosis II / diagnosis
  • Mucopolysaccharidosis II / surgery*
  • Plastic Surgery Procedures / methods*
  • Sternotomy / methods*
  • Tomography, X-Ray Computed
  • Trachea / surgery*
  • Vascular Surgical Procedures / methods*
  • Young Adult