Desmoplastic small round cell tumor of the kidney with unusual imaging features

Meryle J Eklund; Caitlin Cundiff; Bahig M Shehata; Adina L Alazraki

doi:10.1016/j.clinimag.2015.05.002

Desmoplastic small round cell tumor of the kidney with unusual imaging features

Clin Imaging. 2015 Sep-Oct;39(5):904-7. doi: 10.1016/j.clinimag.2015.05.002. Epub 2015 May 7.

Authors

Meryle J Eklund¹, Caitlin Cundiff², Bahig M Shehata³, Adina L Alazraki⁴

Affiliations

¹ Department of Radiology and Imaging Sciences, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: meryle.j.eklund@gmail.com.
² Department of Pathology, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: Caitlin.cundiff@gmail.com.
³ Department of Pathology and Pediatrics, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: bshehat@emory.edu.
⁴ Department of Radiology and Imaging Sciences, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: Adina.alazraki@choa.org.

PMID: 26093512
DOI: 10.1016/j.clinimag.2015.05.002

Abstract

Desmoplastic small round cell tumor (DSRCT) is a rare, high-grade sarcoma seen in children and young adults. DSRCT of the kidney is extremely uncommon, but has been described in both pediatric and adult populations. Here we present an unusual manifestation of renal DSRCT in a boy whose imaging studies revealed a well-circumscribed mass confined to the urinary collecting system, rather than a large aggressive-appearing mass typically associated with DSRCT, which highlights the varied clinical and imaging features of this disease.

Keywords: Desmoplastic small round cell tumor; Pediatric radiology; Renal tumor; t(11;22) (p 13;q 12).

Publication types

Case Reports

MeSH terms

Child
Desmoplastic Small Round Cell Tumor / diagnosis*
Diagnosis, Differential
Diagnostic Imaging / methods*
Humans
Kidney / diagnostic imaging
Kidney / pathology
Kidney Neoplasms / diagnosis*
Magnetic Resonance Imaging / methods*
Male
Tomography, X-Ray Computed
Ultrasonography