[Choroid plexus tumours in childhood: Experience in Sant Joan de Déu hospital]

Abstract

Choroid plexus tumours are rare, with a peak incidence in the first two years of life. The most common location is the lateral ventricle in children, while in adults it is the fourth ventricle. The most common clinical manifestation is the signs and symptoms of intracranial hypertension. They are histologically classified as plexus papilloma, atypical plexus papilloma, and plexus carcinoma. A review is presented on choroid plexus tumours treated in the Hospital Sant Joan de Déu between 1980 and 2014. A total of 18 patients have been treated. An analysis was made of the demographic, clinical, histological data, treatment, and recurrences. The treatment of choice is complete resection, accompanied by adjuvant therapy in carcinomas. In atypical papillomas, the use of adjuvant therapies is controversial, reserving radiation therapy for recurrences. Papillomas have a good outcome, whereas atypical papillomas and carcinomas outcome is poor.

Keywords: Atypical choroid plexus papilloma; Choroid plexus carcinoma; Choroid plexus papilloma; Hidrocefalia; Hydrocephalus; Papiloma atípico de plexo coroideo; Papiloma de plexo coroideo; Tumor de plexo coroideo.