A case of cardiac rhabdomyoma diagnosed during the neonatal period is presented. The condition remitted spontaneously, as was observed by monitoring its course both clinically and by echocardiography. Surgical treatment of this rare condition should be assessed with care, both because of the risk involved in surgery and because of the possibility of a spontaneous cure in rhabdomyomas, which are usually grouped together, as in our case, in a general picture of tuberous sclerosis.