[Diagnosis of a case with Williams-Beuren syndrome by single nucleotide polymorphism array]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2015 Aug;32(4):529-32. doi: 10.3760/cma.j.issn.1003-9406.2015.04.018.
[Article in Chinese]

Abstract

Objective: To explore the genetic cause for a child with mental retardation, developmental delay and multi-systemic developmental disorders by analyzing the copy number variations (CNVs) and correlating the genotype with the phenotype.

Methods: Routine G-banding was performed to analyze the karyotype of the patient and her parents. In addition, single nucleotide polymorphisms array (SNP-array) was used to determine the CNVs, which was confirmed by fluorescence in situ hybridization (FISH).

Results: No karyotypic abnormality was detected upon chromosome analysis. However, SNP-array has identified a de novo hemizygous deletion of 1673 kb on chromosome region 7q11.23, which has been associated with Williams-Beuren syndrome. The microdeletion was confirmed by FISH testing.

Conclusion: A child with Williams-Beuren syndrome has been diagnosed by SNP-array and FISH. The de novo 7q11.23 microdeletion probably underlies the clinical manifestation of the patient. Compared with routine karyotype analysis, SNP-array is more useful for diagnosing children with multiple congenital anomalies with unclear etiology.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Asian People / genetics
  • Child, Preschool
  • China
  • Chromosome Banding
  • Chromosomes, Human, Pair 7 / genetics
  • DNA Copy Number Variations
  • Female
  • Humans
  • Karyotyping
  • Male
  • Pedigree
  • Polymorphism, Single Nucleotide
  • Williams Syndrome / diagnosis
  • Williams Syndrome / genetics*