Diagnostic approach in lymphoplasmacytic plaque

J Eur Acad Dermatol Venereol. 2015 Nov;29(11):2206-15. doi: 10.1111/jdv.13213. Epub 2015 Sep 14.

Abstract

Background: Lymphoplasmacytic plaque (LPP) is a recently described rare skin disease characterized by a dense dermal lymphohistiocytic infiltrate with polyclonal plasma cells. The clinical picture is distinct with reddish to brownish plaque with a predilection for the lower leg. LPP typically affects children.

Objective: To define clinical and histologic criteria of LPP and to develop a diagnostic flow chart.

Methods: We investigated six of our own LPP cases. Immunoglobulin light chains, IgG, IgG4, CD31, CD163 as a histiocytic marker were examined by immunohistochemistry. PCR-based molecular studies were conducted for borrelia sp., mycobacterial and leishmania sp. Moreover, 10 cases, which have been reported in the literature, were checked for the same features.

Results: We could differentiate three main histological patterns (superficial band-like only, [deep] dermal only and mixed). Acanthosis and interface dermatitis are key features in cases with a superficial band-like or mixed infiltrate. Granulomas and giant cells could be only found in about 30% of the cases. The number of plasma cells was variable accounting for 5-40% of the infiltrate. The number of blood vessels was increased in the majority of the cases. 'Free-floating' collagen bundles surrounded by histiocytes (pseudorosettes) were identified as a new histological feature. An infectious agent could be excluded in all cases.

Conclusions: LPP is a long-standing skin disease, which may also occur in adults and in other body regions than the lower leg. Reproducible clinical and histological criteria allow delineating a diagnostic work-up for LPP.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Aged
  • Antigens, CD / analysis
  • Antigens, Differentiation, Myelomonocytic / analysis
  • Blood Vessels / pathology
  • Borrelia burgdorferi / genetics
  • Borrelia burgdorferi / isolation & purification*
  • Child
  • Child, Preschool
  • Collagen / ultrastructure
  • DNA, Bacterial / analysis*
  • DNA, Protozoan / analysis*
  • Female
  • Humans
  • Immunoglobulin G / analysis
  • Immunoglobulin Light Chains / analysis
  • Leishmania / genetics
  • Leishmania / isolation & purification*
  • Male
  • Middle Aged
  • Mycobacterium / genetics
  • Mycobacterium / isolation & purification*
  • Plasma Cells / pathology
  • Platelet Endothelial Cell Adhesion Molecule-1 / analysis
  • Receptors, Cell Surface / analysis
  • Skin / blood supply
  • Skin / chemistry*
  • Skin Diseases / metabolism*
  • Skin Diseases / pathology*
  • Young Adult

Substances

  • Antigens, CD
  • Antigens, Differentiation, Myelomonocytic
  • CD163 antigen
  • DNA, Bacterial
  • DNA, Protozoan
  • Immunoglobulin G
  • Immunoglobulin Light Chains
  • Platelet Endothelial Cell Adhesion Molecule-1
  • Receptors, Cell Surface
  • Collagen