A case of mixed connective tissue disease with pseudo-pseudo Meigs' syndrome (PPMS)-like features

Lupus. 2016 Feb;25(2):214-6. doi: 10.1177/0961203315606441. Epub 2015 Sep 15.

Abstract

Pseudo-pseudo Meigs' syndrome (PPMS) has been reported to be a rare presentation of patients with systemic lupus erythematosus (SLE). However, such a presentation is not common in other forms of connective tissue disease. We presented a case of gross ascites, pleural effusion, and marked elevation of CA-125 level (PPMS-like features) that led to a diagnosis of MCTD. The patient responded to systemic steroid therapy.

Keywords: CA-125; Mixed connective tissue disease; pseudo-pseudo Meigs’ syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Anti-Inflammatory Agents / administration & dosage
  • Diagnosis, Differential
  • Female
  • Humans
  • Lupus Erythematosus, Systemic / pathology
  • Meigs Syndrome / diagnosis*
  • Meigs Syndrome / diagnostic imaging
  • Meigs Syndrome / drug therapy
  • Meigs Syndrome / pathology
  • Methylprednisolone / administration & dosage
  • Mixed Connective Tissue Disease / diagnosis*
  • Mixed Connective Tissue Disease / drug therapy
  • Mixed Connective Tissue Disease / pathology
  • Prednisolone / administration & dosage
  • Radiography
  • Raynaud Disease / pathology*

Substances

  • Anti-Inflammatory Agents
  • Prednisolone
  • Methylprednisolone