Langerhans Cell Histiocytosis of the Bone Presenting as Back Pain: An Unusual Diagnosis for a Common Complaint

Conn Med. 2015 Aug;79(7):409-14.

Abstract

Langerhans cell histiocytosis (LCH) is a rare disease entity characterized by histiocyte infiltration of various organ systems with abroad spectrum of clinical manifestations and prognosis, ranging from benign and self-limiting to lethal. We report a case of a healthy 29-year-old male who presented with upper back pain that was unresponsive to over-the-counter analgesics. The painwas eventually attributed to a single lytic lesion at the posterolateral aspect of his seventh rib, consistent with LCH of the bone. Our patient's symptoms subsided without any surgical intervention apart from a biopsy that was performed for diagnostic purposes. His lytic lesion eventually regressed, and he has remained asymptomatic at follow-up. We provide a brief review of literature on diagnostic approach, guidelines, and treatment modalities for adults diagnosed with LCH of the bone, a rare diagnosis most frequently presenting with a common complaint such as back pain.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Back Pain / diagnosis
  • Back Pain / etiology*
  • Biopsy
  • Bone Diseases / complications
  • Bone Diseases / diagnosis*
  • Diagnosis, Differential
  • Follow-Up Studies
  • Histiocytosis, Langerhans-Cell / complications
  • Histiocytosis, Langerhans-Cell / diagnosis*
  • Humans
  • Male
  • Radiography, Thoracic
  • Radionuclide Imaging
  • Ribs / diagnostic imaging
  • Ribs / pathology*
  • Whole Body Imaging