Transcatheter management of mid-aortic syndrome secondary to myofibroma presenting in infancy with severe left ventricular dysfunction: a case report

Cardiol Young. 2016 Apr;26(4):799-801. doi: 10.1017/S1047951115001936. Epub 2015 Oct 8.


In this study, we summarise a case of a myofibroma causing mid-aortic syndrome due to obstruction of the distal thoracic and abdominal aorta leading to severe left ventricular dysfunction. The patient was managed with percutaneous intervention via balloon dilation and stent placement. On follow-up, the patient has normalisation of ventricular function, is off anti-hypertensives, and is being monitored for re-stenosis.

Keywords: Catheterisation; mid-aortic syndrome; myofibroma.

Publication types

  • Case Reports

MeSH terms

  • Angioplasty, Balloon
  • Aorta, Abdominal
  • Aorta, Thoracic
  • Aortic Diseases / etiology*
  • Catheterization
  • Constriction, Pathologic / etiology
  • Humans
  • Infant
  • Male
  • Mediastinal Neoplasms / complications*
  • Myofibroma / complications*
  • Severity of Illness Index
  • Stents
  • Ventricular Dysfunction, Left / etiology*
  • Ventricular Dysfunction, Left / therapy*