Budd-chiari syndrome and renal arterial neurysms due to Behcet disease: a rare association

Pan Afr Med J. 2015 Jun 3;21:84. doi: 10.11604/pamj.2015.21.84.3917. eCollection 2015.


Behcet's disease is a multisystemic vasculitis of unknown etiology with a chronic relapsing course. Vasculitis in Behcet's disease with predominant vascular involvement is the only vasculitis that affects both arteries and veins of any size. Involvement of the renal artery and inferior vena cava is rare among the arteries and veins, respectively. When disease affect the veins, it is in the form of thrombosis. Arterial complications include aneurysms, stenosis and occlusions. Both rupture of arterial aneurysm and occlusion of suprahepatic veins, causing Budd-Chiari syndrome, are associated with a high mortality rate. Vascular involvement is more common in male patients than in female patients. Men and patients with a younger age of onset present with a more severe prognosis. In this case report, we describe a very rare cause of intrarenal arterial aneurysm's rupture with previous Budd-Chiari syndrome due to Behcet's disease and successful angiographic embolization of actively bleeding aneurysm.

Keywords: Behcet´s disease; Budd-Chiari syndrome; aneurysm rupture; renal arterial microaneurysms.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Aneurysm, Ruptured / etiology*
  • Aneurysm, Ruptured / therapy
  • Angiography
  • Behcet Syndrome / complications*
  • Behcet Syndrome / physiopathology
  • Budd-Chiari Syndrome / etiology*
  • Embolization, Therapeutic / methods
  • Humans
  • Male
  • Renal Artery / pathology*