Radiotherapy in Gorlin Syndrome: Can It Be Safe and Effective in Adult Patients?

J Cutan Med Surg. 2016 Mar-Apr;20(2):159-62. doi: 10.1177/1203475415612481. Epub 2015 Oct 23.

Abstract

Gorlin syndrome, also known as nevoid basal cell carcinoma syndrome, is a rare autosomal dominant disorder with multiple manifestations including early onset of cutaneous basal cell carcinomas (BCCs). Radiotherapy has traditionally been contraindicated due to reports of BCC induction. We describe here a patient treated successfully with radiotherapy with no tumour induction at 57 months of follow-up. A comprehensive literature review of radiotherapy outcomes in patients with Gorlin syndrome suggests radiotherapy may be a feasible treatment option for adult patients with treatment refractory lesions or surgical contraindication.

Keywords: Gorlin syndrome; basal cell carcinoma; nevoid basal cell carcinoma syndrome; radiotherapy; secondary malignancy.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Basal Cell Nevus Syndrome / pathology
  • Basal Cell Nevus Syndrome / radiotherapy*
  • Facial Neoplasms / pathology
  • Facial Neoplasms / radiotherapy*
  • Humans
  • Male
  • Skin Neoplasms / pathology
  • Skin Neoplasms / radiotherapy*