Refractory pulmonary artery aneurysm in Behçet's disease

Dong Xie; Chang Chen; Haifeng Wang; Zhifei Xu; Gening Jiang

doi:10.3978/j.issn.2305-5839.2015.09.27

Refractory pulmonary artery aneurysm in Behçet's disease

Ann Transl Med. 2015 Sep;3(16):239. doi: 10.3978/j.issn.2305-5839.2015.09.27.

Authors

Dong Xie¹, Chang Chen¹, Haifeng Wang¹, Zhifei Xu¹, Gening Jiang¹

Affiliation

¹ 1 Department of Thoracic and Cardiovascular Surgery, Shanghai Changzheng Hospital, the Second Military Medical University, Shanghai 200003, China ; 2 Department of Thoracic Surgery, Shanghai Pulmonary Hospital, Tongji University School of Medicine, Shanghai 200433, China.

PMID: 26539456
PMCID: PMC4598455
DOI: 10.3978/j.issn.2305-5839.2015.09.27

Abstract

Pulmonary artery aneurysm (PAA) is a life-threatening complication of Behçet's disease (BD). Massive hemoptysis secondary to PAAs requires emergent endovascular treatments or surgeries. No endovascular occlusion for pulmonary artery trunk has been reported and no therapeutic algorithm exists for the rare disease. We present an endovascular occlusion and a salvage pneumonectomy for a refractory right main PAA in BD, and provide a proposal of a therapeutic algorithm.

Keywords: Behçet’s disease (BD); Hemoptysis; endovascular treatment; pulmonary artery aneurysm (PAA).