A case of staged Norwood procedure for a unique form of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice: first reported case

Gen Thorac Cardiovasc Surg. 2017 Apr;65(4):209-212. doi: 10.1007/s11748-015-0608-x. Epub 2015 Dec 19.

Abstract

We present the first reported case of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice in a neonate in whom successful palliation was performed using two-staged procedure. The first-stage palliation was the bilateral pulmonary artery band at age 2 days. The second-stage palliation was a Norwood procedure concomitant with ASD creation and patch augmentation of the pulmonary artery confluence at 22 days. The patient is doing well, with unobstructed aortic arch and mild truncal valve regurgitation.

Keywords: Hypoplastic right ventricle; Hypoplastic tricuspid valve; Interrupted aortic arch; Norwood; Truncus arteriosus.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple
  • Aorta, Thoracic / abnormalities*
  • Aorta, Thoracic / surgery
  • Coronary Vessel Anomalies / diagnosis
  • Coronary Vessel Anomalies / surgery*
  • Coronary Vessels / diagnostic imaging*
  • Echocardiography
  • Female
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Humans
  • Infant, Newborn
  • Norwood Procedures / methods*
  • Pulmonary Artery / abnormalities
  • Tomography, X-Ray Computed
  • Tricuspid Valve / abnormalities*
  • Tricuspid Valve / surgery
  • Truncus Arteriosus, Persistent / diagnosis
  • Truncus Arteriosus, Persistent / surgery*