[Choroidal neovascularization complicating Best's vitelliform macular dystrophy in a child]

J Fr Ophtalmol. 2016 Jan;39(1):69-73. doi: 10.1016/j.jfo.2015.05.008. Epub 2015 Dec 18.
[Article in French]

Abstract

Introduction: Best's disease is a progressive macular dystrophy, beginning either in childhood or adolescence.

Case study: We report a rare case of choroidal neovascularization complicating vitelliform dystrophy in a child of 8 years with bilateral progressive loss of visual acuity. The ophthalmoscopic examination showed vitelliform lesions in both foveas. Fluorescein angiography confirmed a subretinal neovascular membrane in the left eye. Additional testing also confirmed the diagnosis of Best's disease associated with choroidal neovascularization.

Discussion: Best's vitelliform macular dystrophy is often asymptomatic because visual acuity tends to remain stable for a long time. A sudden loss of vision suggests the occurrence of complications, such as choroidal neovascularization.

Keywords: Angiographie à la fluorescéine; Best's disease; Choroidal neovascularization; Dystrophie vitelliforme; Fluorescein angiography; Macula; Maladie de Best; Néovascularisation choroïdienne; Vitelliform dystrophy.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Choroidal Neovascularization / etiology*
  • Electrooculography
  • Fluorescein Angiography
  • Humans
  • Male
  • Ophthalmoscopy
  • Slit Lamp
  • Tomography, Optical Coherence
  • Visual Acuity
  • Vitelliform Macular Dystrophy / complications*
  • Vitelliform Macular Dystrophy / diagnosis