An Unusual Type of Totally Anomalous Pulmonary Venous Connection to the Superior Cavoatrial Junction

World J Pediatr Congenit Heart Surg. 2016 Jul;7(4):490-3. doi: 10.1177/2150135115603330. Epub 2016 Jan 21.

Abstract

A neonate with cyanosis at birth was found to have a rare type of totally anomalous pulmonary venous connection. The pulmonary veins entered a confluence posterior to the left atrial wall, which drained into the right superior cavoatrial junction. There were no other major structural defects and no evidence of isomerism. Because of the severe cyanosis, and the restrictive nature of the interatrial communication, we performed balloon atrioseptostomy to improve oxygenation. We then achieved successful surgical repair when the baby was aged 7 months.

Keywords: cardiopulmonary bypass; congenital heart defects; congenital heart surgery; totally anomalous pulmonary venous connection.

Publication types

  • Case Reports

MeSH terms

  • Cardiac Surgical Procedures / methods
  • Cyanosis
  • Female
  • Heart Septal Defects, Atrial / surgery*
  • Humans
  • Infant, Newborn
  • Pulmonary Veins / abnormalities*
  • Treatment Outcome