Double-Lumen Aortic Arch: Persistence of the Fifth Aortic Arch

Ann Thorac Surg. 2016 May;101(5):e155-6. doi: 10.1016/j.athoracsur.2015.10.014.


A persistent fifth aortic arch is exceptionally rare. We report a patient with a double-lumen aortic arch in association with a perimembranous ventricular septal defect and Cornelia de Lange syndrome. We also discuss the morphologic consequences of persistent fifth aortic, arch, which may not be limited to the double-lumen aorta but in fact may be more common.

Publication types

  • Case Reports

MeSH terms

  • Aorta, Thoracic / abnormalities*
  • Aorta, Thoracic / pathology
  • De Lange Syndrome / complications*
  • Female
  • Heart Septal Defects, Ventricular / complications*
  • Humans
  • Infant