Recurrent Bilateral Anterior Uveitis with Kikuchi-Fujimoto Disease

Ocul Immunol Inflamm. 2017 Dec;25(6):866-869. doi: 10.1080/09273948.2016.1188966. Epub 2016 Jul 15.

Abstract

Purpose: To report an uncommon case of Kikuchi-Fujimoto disease-associated-uveitis.

Methods: A 31-year-old Caucasian woman with cervical lymphadenitis and Kikuchi-Fujimoto disease recently confirmed by biopsy, complained about unilateral blurry vision. Differential diagnoses, including non-Hodgkin lymphoma, tuberculosis, sarcoidosis, Behçet disease, rheumatoid arthritis, and juvenile idiopathic arthritis was performed. We undertook a review of other similar cases found in the literature.

Results: Acute anterior unilateral uveitis was diagnosed, suffering from two recurrences of bilateral anterior uveitis.

Conclusions: Additional reported cases are required to better understand the Kikuchi-Fujimoto disease and the pathogenesis and features of its ocular involvement.

Keywords: Corticosteroids; Kikuchi–Fujimoto; lymphadenopathy; ocular inflammation; uveitis.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Female
  • Histiocytes / pathology
  • Histiocytic Necrotizing Lymphadenitis / complications*
  • Histiocytic Necrotizing Lymphadenitis / diagnosis
  • Humans
  • Lymph Nodes / pathology
  • Recurrence
  • Uveitis, Anterior / diagnosis
  • Uveitis, Anterior / etiology*