A Rare Case of Mitral Valve Prolapse in Endomyocardial Fibrosis

Ann Thorac Surg. 2016 Sep;102(3):e217-e219. doi: 10.1016/j.athoracsur.2016.01.098.


Mitral valve prolapse in endomyocardial fibrosis (EMF) is an unusual entity. Literature search reveals only 1 report of mitral valve prolapse assosiated with EMF. A 32-year-old woman, of African origin, who presented with features of right heart failure, was diagnosed to have mitral valve prolapse of rheumatic origin with severe mitral regurgitation and severe pulmonary hypertension (PAH). Intraoperative findings lead to the diagnosis of EMF. We report this rare case of mitral valve prolapse in EMF, in a geographical area where rheumatic heart disease is endemic, to showcase how a rare manifestation of EMF can be misdiagnosed as that of rheumatic heart disease.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Black or African American
  • Echocardiography / methods*
  • Endomyocardial Fibrosis / complications*
  • Endomyocardial Fibrosis / diagnostic imaging
  • Endomyocardial Fibrosis / surgery
  • Female
  • Follow-Up Studies
  • Heart Failure / diagnosis
  • Heart Failure / etiology
  • Heart Valve Prosthesis Implantation / methods*
  • Humans
  • Hypertension, Pulmonary / etiology
  • Hypertension, Pulmonary / physiopathology
  • Hypertension, Pulmonary / therapy
  • Mitral Valve Prolapse / diagnostic imaging*
  • Mitral Valve Prolapse / etiology
  • Mitral Valve Prolapse / surgery*
  • Rare Diseases
  • Risk Assessment
  • Severity of Illness Index
  • Treatment Outcome