Hydrocephalus in Crouzon's syndrome

Childs Nerv Syst. 1989 Jun;5(3):188-9. doi: 10.1007/BF00272125.


We reviewed 42 cases of Crouzon's syndrome. There were 16 cases with ventricular dilation. We believe that shunt should be inserted after fronto-orbital advancement if there are persistent signs of raised intracranial pressure. However, in cases presenting with severe ventricular dilation and papilloedema, a shunt is inserted prior to fronto-orbital advancement. Medium- or high-pressure systems should be used.

MeSH terms

  • Cerebrospinal Fluid Shunts
  • Craniofacial Dysostosis / complications*
  • Craniofacial Dysostosis / diagnostic imaging
  • Craniofacial Dysostosis / psychology
  • Humans
  • Hydrocephalus / diagnostic imaging
  • Hydrocephalus / etiology*
  • Hydrocephalus / surgery
  • Neuropsychological Tests
  • Tomography, X-Ray Computed